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Q75 Other congenital malformations of skull and face bones

ICD-10-CM category Q75 sits in Chapter 17 (Congenital malformations, deformations and chromosomal abnormalities, Q00-Q99). It contains 22 billable codes for FY2027, effective October 1, 2026 to September 30, 2027. Always code to the most specific code available: a code with more characters that describes the diagnosis more precisely takes priority over a shorter one.

Subcategories

Q75.0 CraniosynostosisQ75.00 Craniosynostosis, unspecifiedQ75.02 Coronal craniosynostosisQ75.04 Lambdoid craniosynostosisQ75.05 Multi-suture craniosynostosis

Billable codes in Q75

CodeDescription
Q75.001Craniosynostosis, unspecified type, unilateral
Q75.002Craniosynostosis, unspecified type, bilateral
Q75.009Craniosynostosis, unspecified
Q75.01Sagittal craniosynostosis
Q75.021Coronal craniosynostosis, unilateral
Q75.022Coronal craniosynostosis, bilateral
Q75.029Coronal craniosynostosis, unspecified
Q75.03Metopic craniosynostosis
Q75.041Lambdoid craniosynostosis, unilateral
Q75.042Lambdoid craniosynostosis, bilateral
Q75.049Lambdoid craniosynostosis, unspecified
Q75.051Cloverleaf skull
Q75.052Pansynostosis
Q75.058Other multi-suture craniosynostosis
Q75.08Other single-suture craniosynostosis
Q75.1Craniofacial dysostosis
Q75.2Hypertelorism
Q75.3Macrocephaly
Q75.4Mandibulofacial dysostosis
Q75.5Oculomandibular dysostosis
Q75.8Other specified congenital malformations of skull and face bones
Q75.9Congenital malformation of skull and face bones, unspecified

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