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E76 Disorders of glycosaminoglycan metabolism

ICD-10-CM category E76 sits in Chapter 4 (Endocrine, nutritional and metabolic diseases, E00-E89). It contains 12 billable codes for FY2027, effective October 1, 2026 to September 30, 2027. Always code to the most specific code available: a code with more characters that describes the diagnosis more precisely takes priority over a shorter one.

Subcategories

E76.0 Mucopolysaccharidosis, type IE76.2 Other mucopolysaccharidosesE76.21 Morquio mucopolysaccharidoses

Billable codes in E76

CodeDescription
E76.01Hurler's syndrome
E76.02Hurler-Scheie syndrome
E76.03Scheie's syndrome
E76.1Mucopolysaccharidosis, type II
E76.210Morquio A mucopolysaccharidoses
E76.211Morquio B mucopolysaccharidoses
E76.219Morquio mucopolysaccharidoses, unspecified
E76.22Sanfilippo mucopolysaccharidoses
E76.29Other mucopolysaccharidoses
E76.3Mucopolysaccharidosis, unspecified
E76.8Other disorders of glucosaminoglycan metabolism
E76.9Glucosaminoglycan metabolism disorder, unspecified

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